摘要
A型血友病是罕见的X连锁隐性遗传病,可表现为全身任何部位自发性或轻微创伤后长时间过度出血^([1])。作为下肢重要负重关节的膝关节极易受累^([2])。关节腔内进行性反复出血可引发慢性疼痛、关节畸形,甚至致残,严重降低患者生活质量^([3])。全膝关节置换术(total knee arthroplasty,TKA)是重度血友病性关节炎患者的有效治疗手段^([4])。
作者
安然逊
徐园
王英杰
王钰
朱丽筠
杨旭
尚高鹏
刘佳
李姗姗
李文利
马玉芬
AN Ranxun;XU Yuan;WANG Yingjie;WANG Yu;ZHU Liyun;YANG Xu;SHANG Gaopeng;LIU Jia;LI Shanshan;LI Wenli;MA Yufen(Department of Nursing,Peking Union Medical College Hospital,Chinese Academy of Medical Sciences&Peking Union Medical College,Beijing 100730;Department of Health Care,Peking Union Medical College Hospital,Chinese Academy of Medical Sciences&Peking Union Medical College,Beijing 100730;Department of Orthopaedics,Peking Union Medical College Hospital,Chinese Academy of Medical Sciences&Peking Union Medical College,Beijing 100730;Department of Cardiac Surgery,Peking Union Medical College Hospital,Chinese Academy of Medical Sciences&Peking Union Medical College,Beijing 100730;Department of Gastroenterology,Peking Union Medical College Hospital,Chinese Academy of Medical Sciences&Peking Union Medical College,Beijing 100730;Peking Union Medical College Hospital,Chinese Academy of Medical Sciences and Peking Union Medical College Hospital,Beijing 100730,China)
出处
《中华骨与关节外科杂志》
CSCD
北大核心
2024年第2期165-169,共5页
Chinese Journal of Bone and Joint Surgery
基金
中央高水平医院临床科研专项基金(2022-PUMCH-A-132)。
关键词
血友病性关节炎
全膝关节置换术
跨理论模型
疾病管理
Hemophilic Arthropathy
Total Knee Arthroplasty
Trans-theoretical Model
Disease Management
作者简介
通信作者:马玉芬,Email:yumafen@126.com。