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NEW SIMPLE SMOOTH MERIT FUNCTION FOR BOX CONSTRAINED VARIATIONAL INEQUALITIES AND DAMPED NEWTON TYPE METHOD 被引量:3
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作者 乌力吉 陈国庆 《应用数学和力学》 EI CSCD 北大核心 2005年第8期988-996,共9页
By introducing a smooth merit function for the median function, a new smooth merit function for box constrained variational inequalities (BVIs) was constructed. The function is simple and has some good differential pr... By introducing a smooth merit function for the median function, a new smooth merit function for box constrained variational inequalities (BVIs) was constructed. The function is simple and has some good differential properties. A damped Newton type method was presented based on it.Global and local superlinear/quadratic convergence results were obtained under mild conditions, and the finite termination property was also shown for the linear BVIs. Numerical results suggest that the method is efficient and promising. 展开更多
关键词 箱约束变分不等式 全局收敛 超线性收敛 有限步收敛
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Variational analysis of mid-span deflection of gantry cranes 被引量:3
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作者 ZHANG Da-peng CHENG Wen-ming WANG Bin 《Journal of Central South University》 SCIE EI CAS CSCD 2017年第11期2705-2716,共12页
In practical application, it is very important to master the influence of structure parameters on the mid-span deflection quantificationally. For large-span and heavy-duty gantry cranes, the influence of the rigid leg... In practical application, it is very important to master the influence of structure parameters on the mid-span deflection quantificationally. For large-span and heavy-duty gantry cranes, the influence of the rigid leg and the soft leg on mid-span deflection has not been considered in the past. In the paper, the mathematical model is established for universal large-span and heavy-duty gantry cranes. The analytical solution for the mid-span deflection of gantry-frame structure girder is derived and obtained based on the variation principle by considering the coupling effect of the bending moments of girder and legs, the axial force and the secondary bending moments. The relation between the load and the deflection on the mid-span of the gantry-frame structure girder is known. Then, the experimental model is designed according to dimensional analysis method. And experiments were performed on the WEW-600 B type testing machine. Hackling experimental data, the regular of the load and deflection on the girder mid-span is obtained, namely, the deformation of the gantry-frame structure resists the external load to do work. The validity of the nonlinear analytical solution of the girder deflection is verified. Experimental results show that the analytical solution of the gantry-frame structure deflection has much higher calculation accuracy than previous calculation method. This work provides a theoretical basis for the design and inspection of gantry-frame structures. 展开更多
关键词 GANTRY CRANE DEFLECTION STRUCTURAL STIFFNESS variational analysis
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Adaptive variational models for image decomposition combining staircase reduction and texture extraction 被引量:1
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作者 Jiang Lingling Yin Haiqing Feng Xiangchu 《Journal of Systems Engineering and Electronics》 SCIE EI CSCD 2009年第2期254-259,共6页
New models for image decomposition are proposed which separate an image into a cartoon, consisting only of geometric objects, and an oscillatory component, consisting of textures or noise. The proposed models are give... New models for image decomposition are proposed which separate an image into a cartoon, consisting only of geometric objects, and an oscillatory component, consisting of textures or noise. The proposed models are given in a variational formulation with adaptive regularization norms for both the cartoon and texture parts. The adaptive behavior preserves key features such as object boundaries and textures while avoiding staircasing in what should be smooth regions. This decomposition is computed by minimizing a convex functional which depends on the two variables u and v, alternatively in each variable. Experimental results and comparisons to validate the proposed models are presented. 展开更多
关键词 image decomposition total variation minimization bounded variation TEXTURE
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Plastic variational principle based on the least work consumption principle 被引量:1
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作者 唐松花 罗迎社 +1 位作者 周筑宝 王智超 《Journal of Central South University》 SCIE EI CAS 2008年第S1期39-42,共4页
Plastic variational principles are foundation to solve the boundary-value problems of plastic mechanics with the variational method(or energy method) and finite element method.The most convenient way of establishing d... Plastic variational principles are foundation to solve the boundary-value problems of plastic mechanics with the variational method(or energy method) and finite element method.The most convenient way of establishing different kinds of variational principles is to set up the extreme principle related to the studied problem.Based on a general new extreme principle-the Least work consumption principle,the variational principles of the rigid-plastic and rigid-viscoplastic material were derived.In comparison with existing methods,the method in this paper is more clear and direct,and the physical meaning is clear-cut.This method can offer a new way for establishing other kinds of variational principles. 展开更多
关键词 RIGID-PLASTIC rigid-viscoplastic variational PRINCIPLE the least work CONSUMPTION PRINCIPLE
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A Variational Method for the Fuse-Warhead Coordination Design of an Air-Faced Missile 被引量:2
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作者 Gao Peiwang(Department of Engineering Safety, Beijing Institute of Technology, 100081, P. R. China)Miao Ligong(Beijing Institute of Electronic System Engineering, 100854, P. R. China)Yao Cuiyou & Ma Xiaoqing(Department of Engineering Safety, Beijing Insti 《Journal of Systems Engineering and Electronics》 SCIE EI CSCD 1999年第4期72-80,共9页
This paper presents a variational method for the fuse-warhead coordination design of an air-faced missile, which takes the distribution density of fragments for a variable and the totalprobability of kill of single mi... This paper presents a variational method for the fuse-warhead coordination design of an air-faced missile, which takes the distribution density of fragments for a variable and the totalprobability of kill of single missile against an air-target for an objective function. 展开更多
关键词 Air-faced missile Fuse-warhead coordination Kill probability of single against an airtarget variational calculus
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Modeling and solving for transverse vibration of gear with variational thickness 被引量:6
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作者 QIN Hui-bin LU Ming +2 位作者 SHE Yin-zhu WANG Shi-ying LI Xiang-peng 《Journal of Central South University》 SCIE EI CAS 2013年第8期2124-2133,共10页
A analyzed model of gear with wheel hub, web and rim was derived from the Mindlin moderate plate theory. The gear was divided into three annular segments along the locations of the step variations. Traverse displaceme... A analyzed model of gear with wheel hub, web and rim was derived from the Mindlin moderate plate theory. The gear was divided into three annular segments along the locations of the step variations. Traverse displacement, rotation angle, shear force and fiexural moment were equal to ensure the continuity along the interface of the wheel hub, web and rim segments. The governing differential equations for harmonic vibration of annular segments were derived to solve the gear vibration problem. The influence of hole to diameter ratios, segment thickness ratios, segment location ratios, Poisson ratio on the vibration behavior of stepped circular Mindlin disk were calculated, tabletted and plotted. Comparisons were made with the frequencies arising from the presented method, finite elements method, and structure modal experiment. The result correlation among these three ways is very good. The largest error for all frequencies is 5.46%, and less than 5% for most frequencies. 展开更多
关键词 gear with variational thickness Mindlin moderately plate theory transverse and flexural vibration model resonantfrequencies of vibration
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Astronomical image restoration using variational Bayesian blind deconvolution
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作者 Xiaoping Shi Rui Guo +1 位作者 Yi Zhu Zicai Wang 《Journal of Systems Engineering and Electronics》 SCIE EI CSCD 2017年第6期1236-1247,共12页
An algorithm is presented for image prior combinations based blind deconvolution and applied to astronomical images.Using a hierarchical Bayesian framework, the unknown original image and all required algorithmic para... An algorithm is presented for image prior combinations based blind deconvolution and applied to astronomical images.Using a hierarchical Bayesian framework, the unknown original image and all required algorithmic parameters are estimated simultaneously. Through utilization of variational Bayesian analysis,approximations of the posterior distributions on each unknown are obtained by minimizing the Kullback-Leibler(KL) distance, thus providing uncertainties of the estimates during the restoration process. Experimental results on both synthetic images and real astronomical images demonstrate that the proposed approaches compare favorably to other state-of-the-art reconstruction methods. 展开更多
关键词 blind deconvolution variational Bayesian model com bination astronomical image processing
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Forward Affine Point Set Matching Under Variational Bayesian Framework 被引量:1
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作者 QU Han-Bing CHEN Xi +1 位作者 WANG Song-Tao YU Ming 《自动化学报》 EI CSCD 北大核心 2015年第8期1482-1494,共13页
关键词 贝叶斯 点集 匹配 仿射 框架 变分 逼近算法 线性变换
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Underwater acoustic signal denoising model based on secondary variational mode decomposition
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作者 Hong Yang Wen-shuai Shi Guo-hui Li 《Defence Technology(防务技术)》 SCIE EI CAS CSCD 2023年第10期87-110,共24页
Due to the complexity of marine environment,underwater acoustic signal will be affected by complex background noise during transmission.Underwater acoustic signal denoising is always a difficult problem in underwater ... Due to the complexity of marine environment,underwater acoustic signal will be affected by complex background noise during transmission.Underwater acoustic signal denoising is always a difficult problem in underwater acoustic signal processing.To obtain a better denoising effect,a new denoising method of underwater acoustic signal based on optimized variational mode decomposition by black widow optimization algorithm(BVMD),fluctuation-based dispersion entropy threshold improved by Otsu method(OFDE),cosine similarity stationary threshold(CSST),BVMD,fluctuation-based dispersion entropy(FDE),named BVMD-OFDE-CSST-BVMD-FDE,is proposed.In the first place,decompose the original signal into a series of intrinsic mode functions(IMFs)by BVMD.Afterwards,distinguish pure IMFs,mixed IMFs and noise IMFs by OFDE and CSST,and reconstruct pure IMFs and mixed IMFs to obtain primary denoised signal.In the end,decompose primary denoising signal into IMFs by BVMD again,use the FDE value to distinguish noise IMFs and pure IMFs,and reconstruct pure IMFs to obtain the final denoised signal.The proposed mothod has three advantages:(i)BVMD can adaptively select the decomposition layer and penalty factor of VMD.(ii)FDE and CS are used as double criteria to distinguish noise IMFs from useful IMFs,and Otsu algorithm and CSST algorithm can effectively avoid the error caused by manually selecting thresholds.(iii)Secondary decomposition can make up for the deficiency of primary decomposition and further remove a small amount of noise.The chaotic signal and real ship signal are denoised.The experiment result shows that the proposed method can effectively denoise.It improves the denoising effect after primary decomposition,and has good practical value. 展开更多
关键词 Underwater acoustic signal DENOISING variational mode decomposition Secondary decomposition Fluctuation-based dispersion entropy Cosine similarity
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Analytical solution to mapping rail deformation under bridge transverse deformation using energy variational principle
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作者 LAI Zhi-peng JIANG Li-zhong +3 位作者 ZHOU Wang-bao LIU Xiang YU Jian ZHANG Yun-tai 《Journal of Central South University》 SCIE EI CAS CSCD 2022年第8期2654-2664,共11页
The track geometry is a critical factor that affects the running safety and riding comfort of trains moving on a high-speed railway bridge.This study addresses the mapping relationship between the track deformation an... The track geometry is a critical factor that affects the running safety and riding comfort of trains moving on a high-speed railway bridge.This study addresses the mapping relationship between the track deformation and lateral deformations of bridges.Equilibrium equations and natural boundary conditions of the track-bridge system are established based on the energy variational principle,and an analytical solution is derived for the track deformation accounting for lateral bridge deformations.A five-span simply-supported bridge with continuous welded rail has been selected as the case study.The mapping rail deformations are compared to the finite element results,and both results agree well with each other,validating the analytical method proposed in this paper.The influence factors on the mapping rail deformation are further evaluated.Results show that the mapping rail deformation is consistent with the girder displacement at the area that is away from the girder ends when the flexural stiffness ratio between the track and the bridge girder is low.The interlayer stiffness has a significant effect on the mapping rail deformation when the track flexural stiffness is of a high value. 展开更多
关键词 energy variational principle simply-supported beam bridge high-speed railway continuous welded rail mapping rail deformation
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Perceptual Contrast-Based Image Fusion: A Variational Approach 被引量:6
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作者 WANG Chao YE Zhong-Fu 《自动化学报》 EI CSCD 北大核心 2007年第2期132-137,共6页
本地对比,或变化,在主要是从来源图象保存重要信息到熔化结果的图象熔化起一个重要作用。威伯的法律告诉我们在不同背景下面的一样的变化将引起不同感性的感情,因此,一个理想的图象处理器不得不考虑视觉心理学和心物学的效果。这份... 本地对比,或变化,在主要是从来源图象保存重要信息到熔化结果的图象熔化起一个重要作用。威伯的法律告诉我们在不同背景下面的一样的变化将引起不同感性的感情,因此,一个理想的图象处理器不得不考虑视觉心理学和心物学的效果。这份报纸考虑人的视觉系统(HVS ) 的性质并且从每幅来源图象把量的感性的变化转移到结果。把 just-noticeable-difference (JND ) 用作测量, multiband 图象的感性的对比作为一个目标被获得。我们构造一个功能的极值问题发现一幅单身的乐队图象,或熔化结果,它有最近感性的对比到目标一个。经由变化途径, Euler-Lagrange 方程被导出,并且一次坡度降下重复被采用。试验性的结果证明这个方法感性地好。 展开更多
关键词 表象聚变 变化方法 知觉衬比度 HVS PDES 人工智能
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Variational calculation of the Intrashell 2p^2 ~3P^e State for Heliumlike F^( 7+) ion
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作者 GUANG Xiao xu 1, WANG Zhi wen(Z.W.Wang) 2(1.Wuhan Institute of Physics and Mathematics, Chinese Academy of Science, Wuhan 430071 2.Department of Physics,Liaoning Normal University, Dalian 116029) 《原子与分子物理学报》 CAS CSCD 北大核心 2000年第4期743-747,共5页
Doubly excited intrashell 2p 2 3P e state in heliumlike F 7+ ion is calculated by using the modified configuration interaction wave function. Using the modified Slater type wave function having up to 362 terms, the en... Doubly excited intrashell 2p 2 3P e state in heliumlike F 7+ ion is calculated by using the modified configuration interaction wave function. Using the modified Slater type wave function having up to 362 terms, the energy position of the discrete 2p 2 3P e state in F 7+ is determined to be -18.812 629 78 a.u., Several expectation values of r i,r -1 12 and r 12 are also given in the present work. The present results indicate that the modified Slater type wave function in which r < and r > coordinates are incorporated is effective and powerful for the description of the 2p 2 3P e state showing strong correlation effect in two electron systems. 展开更多
关键词 变分计算 壳层 氟离子 氦状态
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GNSS spoofing detection for single antenna receivers via CNR variation monitoring
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作者 LIAO Maoyou LYU Xu +1 位作者 MENG Ziyang YOU Zheng 《Journal of Systems Engineering and Electronics》 SCIE CSCD 2024年第5期1276-1286,共11页
In this paper,a method for spoofing detection based on the variation of the signal’s carrier-to-noise ratio(CNR)is proposed.This method leverages the directionality of the antenna to induce varying gain changes in th... In this paper,a method for spoofing detection based on the variation of the signal’s carrier-to-noise ratio(CNR)is proposed.This method leverages the directionality of the antenna to induce varying gain changes in the signals across different incident directions,resulting in distinct CNR variations for each signal.A model is developed to calculate the variation value of the signal CNR based on the antenna gain pattern.This model enables the differentiation of the variation values of the CNR for authentic satellite signals and spoofing signals,thereby facilitating spoofing detection.The proposed method is capable of detecting spoofing signals with power and CNR similar to those of authentic satellite signals.The accuracy of the signal CNR variation value calculation model and the effectiveness of the spoofing detection method are verified through a series of experiments.In addition,the proposed spoofing detection method works not only for a single spoofing source but also for distributed spoofing sources. 展开更多
关键词 spoofing detection global navigation satellite system(GNSS) variation of carrier-to-noise ratio(CNR) antenna directionality
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10年生台湾桤木木材纤维形态变异规律研究 被引量:1
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作者 刘晓玲 禤示青 +3 位作者 曹艳云 陈桂丹 黄志玲 陈松武 《林产工业》 北大核心 2025年第3期12-18,共7页
针对生长迅速且易加工的台湾桤木,以10年生树木为样本,深入分析其木材纤维形态在纵向与径向上的变异规律。结果表明:台湾桤木的木材纤维形态径向变异较纵向更为显著。随树木高度的增加,纤维长度和纤维长宽比呈现波动性下降,而纤维宽度... 针对生长迅速且易加工的台湾桤木,以10年生树木为样本,深入分析其木材纤维形态在纵向与径向上的变异规律。结果表明:台湾桤木的木材纤维形态径向变异较纵向更为显著。随树木高度的增加,纤维长度和纤维长宽比呈现波动性下降,而纤维宽度、腔径、双壁厚和壁腔比增减幅度不大。自髓心向外,纤维长度、宽度、长宽比和双壁厚均呈现逐渐增加的变异规律,且南向心材优于北向心材,而过渡材和边材的结果与之相反。此外,各纤维形态间的相关性分析表明,纤维长度与长宽比、纤维宽度与腔径呈现极显著的正相关关系,纤维宽度与双壁厚呈现显著正相关关系,而纤维壁腔比与宽度、腔径则呈现了极显著的负相关关系。10年生台湾桤木木材纤维形态变异规律为其合理加工利用提供了重要理论依据。 展开更多
关键词 台湾桤木 纤维形态 纵向变异 径向变异 相关性分析
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季节性气象因子对生活垃圾填埋场甲烷释放的影响 被引量:1
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作者 卞荣星 滕晓 +6 位作者 孙治国 朱润泽 牛亚婷 杜欣然 高淑丹 刘克琼 孙英杰 《中国环境科学》 北大核心 2025年第4期2008-2015,共8页
为明确填埋场甲烷释放的时空变化规律及其影响机制,以青岛某生活垃圾填埋场为例,采用静态箱法测定了不同季节甲烷释放通量日动态变化.结果表明,填埋场甲烷释放通量季节变化显著,冬季释放最高为(115.67±65.34)mmol/(m^(2)·h),... 为明确填埋场甲烷释放的时空变化规律及其影响机制,以青岛某生活垃圾填埋场为例,采用静态箱法测定了不同季节甲烷释放通量日动态变化.结果表明,填埋场甲烷释放通量季节变化显著,冬季释放最高为(115.67±65.34)mmol/(m^(2)·h),夏季释放最低为(61.51±74.57)mmol/(m^(2)·h).不同季节的日甲烷释放通量存在明显差异,夏季甲烷释放通量呈现双峰曲线,秋冬季甲烷释放通量呈现单峰曲线.相关性分析表明甲烷释放通量与大气压、大气温度、大气相对湿度、风速、土壤温度、土壤相对湿度显著相关;夏秋季甲烷释放通量与大气相对湿度和大气温度分别呈显著正相关和负相关,而冬季则相反. 展开更多
关键词 甲烷释放 生活垃圾填埋场 气象因子 季节变化 日变化
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1956-2016年中国降水量时空分布规律及变化特征 被引量:3
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作者 李原园 李云玲 +2 位作者 郭旭宁 潘扎荣 刘为锋 《水科学进展》 北大核心 2025年第1期1-17,共17页
为应对气候变化背景下降水时空演变对经济社会发展和生态环境保护带来的挑战,基于第三次全国水资源调查评价1956—2016年逐月降水量观测数据,全面剖析了降水量在全国、水资源一级区、省级行政区的空间分布规律以及年际变化、年内分配等... 为应对气候变化背景下降水时空演变对经济社会发展和生态环境保护带来的挑战,基于第三次全国水资源调查评价1956—2016年逐月降水量观测数据,全面剖析了降水量在全国、水资源一级区、省级行政区的空间分布规律以及年际变化、年内分配等时间分布特征,探讨了降水时空分布的变化趋势。结果表明:中国南方地区多年平均年降水深为1215.1 mm,北方地区仅为329.3 mm;各水资源一级区均出现连枯连丰现象,降水量越少的区域年际变化越显著;北方地区连续最大4个月降水量占多年平均年降水量的70%~80%,南方地区则占50%~65%;1956—2016年全国降水量呈现出丰枯交替的现象,整体变化趋势未发生明显变化。 展开更多
关键词 降水量 时空分布 年际变化 年内分配 变化趋势
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1961—2023年中国降雨侵蚀力变化特征及未来趋势预估 被引量:1
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作者 高歌 陈涛 徐沅鑫 《农业工程学报》 北大核心 2025年第4期50-58,共9页
为水土流失预防和科学治理提供参考,基于1961—2023年中国均一化逐日降水资料对降雨侵蚀力进行估算,并结合侵蚀性降雨特征开展降雨侵蚀力变化趋势和成因分析,并探讨降雨侵蚀力的极端变化,在此基础上,摸清中国及十大流域降雨侵蚀力变化... 为水土流失预防和科学治理提供参考,基于1961—2023年中国均一化逐日降水资料对降雨侵蚀力进行估算,并结合侵蚀性降雨特征开展降雨侵蚀力变化趋势和成因分析,并探讨降雨侵蚀力的极端变化,在此基础上,摸清中国及十大流域降雨侵蚀力变化危险状况,并基于Hurst方法预估未来变化趋势。结果表明:1)1961—2023年,中国及东南诸河、西北诸河流域年降雨侵蚀力呈现显著增加趋势,西南诸河流域则呈现显著减少趋势,其余大多数流域增加趋势不明显;2)中国及十大流域大多年侵蚀性降雨量、雨日、平均降雨强度增加,其中平均降雨强度和/或降雨量的变化为大多数流域年降雨侵蚀力变化的主要成因;3)中国大部地区年最大日降雨侵蚀力增加,10年一遇次降雨侵蚀力1961—2023年相比1961—1990年呈增加的站点比例多达64.3%;4)近60年来,中国大部地区降雨侵蚀力变化具有危险性,站点比例达80%,其中降雨侵蚀力总量及极端都呈增加变化的类型在各流域均最为突出、范围最大;5)除西南诸河流域外,预估大多数流域年降雨侵蚀力未来变化趋势将均以持续增加为主。目前和未来气候条件对中国水土流失治理不容乐观,需根据降雨侵蚀力变化特点,因地制宜制定长期规划和采取有效措施。 展开更多
关键词 降雨 侵蚀 变化 极端 趋势预估
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计及电网参数不平衡的灵活接地系统高阻接地故障选线方法 被引量:2
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作者 李晓波 张世乐 +3 位作者 谢剑锋 彭超红 刘栩鹏 梁睿 《电力系统保护与控制》 北大核心 2025年第5期59-68,共10页
灵活接地系统采用的零序过电流保护存在耐过渡电阻能力低的问题,并且现有的选线方法对互感器精度要求较高,也未考虑电网参数不平衡对判据的影响,存在保护误判的风险。针对上述问题,首先在计及电网参数不平衡条件下,探究了并联小电阻投... 灵活接地系统采用的零序过电流保护存在耐过渡电阻能力低的问题,并且现有的选线方法对互感器精度要求较高,也未考虑电网参数不平衡对判据的影响,存在保护误判的风险。针对上述问题,首先在计及电网参数不平衡条件下,探究了并联小电阻投入前后各电气信号变化量与线路对地参数、不平衡电流的关系。研究发现健全线路零序电流变化量与零序电压变化量之比等于该线路对地导纳,故障线路的零序电流变化量与零序电压变化量之比则为线路对地导纳与接地导纳的总和。在此基础上,提出了一种适用于灵活接地系统单相高阻接地故障的选线方法。该方法不受电网参数不平衡与零序CT极性反接影响,能够有效降低保护对互感器精度的要求。此外,该方法还可利用故障信息实现电网参数不平衡条件下对过渡电阻及单条线路对地导纳的测量。最后,在搭建的仿真电路中验证了所述方法的正确性和有效性。 展开更多
关键词 灵活接地系统 电网参数不平衡 零序电压变化量 零序电流变化量 高阻接地故障
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儿童先天性长QT综合征14例临床表型及基因变异分析 被引量:1
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作者 孙琪青 陈蒙蒙 +6 位作者 付大鹏 何坤 燕笑尘 侯维纳 王芳洁 谢振华 李东晓 《临床儿科杂志》 北大核心 2025年第4期278-285,共8页
目的对先天性长QT综合征(LQTS)患儿临床表型及基因变异谱进行总结分析,探讨LQTS基因型与临床表型的潜在相关性。方法选取2018年11月至2023年11月心内科收治的14个无亲缘关系的LQTS家系作为研究对象,收集患儿的临床资料,对患儿进行家系... 目的对先天性长QT综合征(LQTS)患儿临床表型及基因变异谱进行总结分析,探讨LQTS基因型与临床表型的潜在相关性。方法选取2018年11月至2023年11月心内科收治的14个无亲缘关系的LQTS家系作为研究对象,收集患儿的临床资料,对患儿进行家系全外显子组测序,应用Sanger测序验证候选变异,并对患儿进行治疗和随访。结果14例患儿中男6例、女8例,中位发病年龄为82.5(37.5~129.8)个月。14例以心跳骤停、晕厥或阿斯综合征发病。共检出5个基因(KCNQ1、KCNH2、SCN5A、CACNA1C和CALM1基因)的相关变异,依据美国医学遗传学与基因组学学会(ACMG)相关变异评级指南,变异位点均为致病性变异或可能致病性变异。其中,SCN5A基因(NM_198056.2)c.796C>G(p.Leu266Val)变异既往未见文献报道,依据ACMG指南评级为可能致病变异(PS2+PM2_Supporting+PP 3)。14例患儿均用β受体阻滞剂治疗,其中2例联用美西律治疗;随访至2024年3月31日,3例死亡;1例因自行停药而导致阿斯综合征发作1次,余均未再出现晕厥。结论本研究发现了一个SCN5A基因的新变异c.796C>G(p.Leu 266Val),拓展了先天性LQTS相关SCN5A基因变异谱。先天性LQTS发病形式多样,对于疑似LQTS的患儿应进行心电图检查,并结合基因检测可对疾病明确诊断。 展开更多
关键词 先天性长QT综合征 SCN5A基因 变异
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2024年夏季中国气候异常特征及成因分析 被引量:5
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作者 李想 郑志海 《气象》 北大核心 2025年第1期110-121,共12页
2024年夏季,中国降水偏多、气温偏高。全国平均气温22.3℃,为1961年以来历史同期第一,高温天气过程偏早、范围广、极端性强;降水空间分布上呈“东多西少”分布,东北南部、内蒙古中部、华北东部、华东北部、华中北部和西南部、西北地区... 2024年夏季,中国降水偏多、气温偏高。全国平均气温22.3℃,为1961年以来历史同期第一,高温天气过程偏早、范围广、极端性强;降水空间分布上呈“东多西少”分布,东北南部、内蒙古中部、华北东部、华东北部、华中北部和西南部、西北地区东部等地降水较常年同期偏多5成至1倍。夏季台风生成个数和登陆个数均偏少。2023年5月开始的中等强度El Nino事件在2024年5月结束并向冷海温发展,2023/2024年冬季以来,热带印度洋和北大西洋海温均为历史同期最暖,热带三大洋的异常海温分布有利于夏季西太平洋副热带高压增强,将充沛的太平洋和印度洋水汽输送到中国东部,使得东部季风区降水大范围偏多,强降水过程多。 展开更多
关键词 气候异常 季节内变化 西太平洋副热带高压 副热带西风急流
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